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Table 1 Interstitial lung disorders: major categories

From: Diagnosis and management of interstitial lung disease

• Idiopathic interstitial pneumonia

• Sarcoidosis

 o Idiopathic pulmonary   fibrosis (IPF)

• Hypersensitivity pneumonitis

 o Non-specific interstitial   pneumonia (NSIP)

• Iatrogenic pneumonitis/fibrosis (drug-induced ILD, radiation injury)

 o Cryptogenic organizing   pneumonia (COP)

• Eosinophilic ILD (e.g. eosinophilic pneumonia)

 o Respiratory bronchiolitis   interstitial lung disease (RBILD)

• Occupational lung disease

 o Desquamative interstitial   pneumonia (DIP)

• Inherited disorders (e.g. familial pulmonary fibrosis, Hermansky-Pudlak syndrome)

 o Acute interstitial   pneumonia (AIP)

• Primary disorders (e.g. pulmonary Langerhans cell histiocytosis)

 o Lymphoid interstitial   pneumonia (LIP)

 

• Connective tissue disease-associated interstitial lung disease (CTD-ILD)

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