Organ system | Finding | Associated ILD or its complications |
---|---|---|
Lung | Velcro crackles | IPF, asbestosis > > other |
Squeaks | HP, bronchiolitis | |
Pleural rub | RA, SLE | |
Skin | Erythema nodosum | Sarcoidosis, CTD, Behçet’s disease |
Maculopapular rash | CVD, drugs, sarcoidosis, amyloid | |
Heliotrope rash | DM-PM | |
Gottron’s papules | DM-PM | |
Café-au-lait spots | Neurofibromatosis | |
Albinism | HPS | |
Telangiectasia | Scleroderma | |
Calcinosis | Scleroderma, DM-PM | |
Subcutaneous nodules | RA, neurofibromatosis, vasculitis | |
Cutaneous vasculitis | PAG, RA, MPA, SLE, drug reaction | |
Mechanic’s hands | DM-PM | |
Tight skin/ulcerations over digits | Scleroderma | |
Eyes | Uveitis | Sarcoidosis, Behçet’s disease, AS |
Scleritis | SLE, scleroderma, sarcoidosis, PAG | |
Keratoconjunctivitis sicca | Sjögren’s disease, CTD | |
Lacrimal gland enlargement | Sarcoidosis | |
Horizontal nystagmus | HPS | |
Salivary glands | Enlarged | Sjögren’s disease, sarcoidosis |
Lymphatic | Lymphadenopathy | Sarcoidosis, lymphangitic CA, lymphoma |
Reticuloendothelial | Hepatosplenomegaly | Sarcoidosis, LIP, CTD, EG, amyloid, lymphoma |
Musculoskeletal | Muscle weakness, myositis | CTD (especially DM-PM), sarcoidosis |
Synovitis, arthritis | CTD, sarcoidosis | |
Nervous system | Neurologic dysfunction | Sarcoidosis, lymphangitic CA, NF, TS, CTD, PAG, MPA |
Cardiovascular | Systemic hypertension | CTD, GPS, PAG, MPA, NF |
Prominent P2 | Suggests secondary PH (IPF, CTD, end stage sarcoidosis) | |
Pericardial rub | Sarcoidosis, SLE | |
Extremities | Digital clubbing | IPF, asbestosis > chronic HP, DIP > other fibrotic ILD |
Raynaud’s phenomenon | CTD |